Term Name:	dentin dysplasia type IA
Synonyms:	atypical dentin dysplasia due to SMOC2 deficiency
Definition:	A dentin dysplasia characterized by oligodontia, microdontia with very globular and malformed teeth and incisal notches, taurodontism of the molar teeth, and short roots that has_material_basis_in homozygous mutation in the SMOC2 gene on chromosome 6q27.
Ontology:	Human Disease [DOID:0070704]   ( DOID:0070704 )